南方医科大学学报

南方医科大学学报 ›› 2013, Vol. 33 ›› Issue (12): 1864-.

• • 上一篇    

伴PNH样缺陷的自身免疫性溶血性贫血1例报告

唐举贤，寇伟，陈琪，肖端   

  • 出版日期:2013-12-20 发布日期:2013-12-20

Autoimmune hemolytic anemia with a paroxysmal nocturnal hemoglobinuria-like defect:
report of one case

  • Online:2013-12-20 Published:2013-12-20

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摘要： 自身免疫性溶血性贫血和阵发性睡眠性血红蛋白尿都是常见的溶血性疾病，前者是由于免疫功能紊乱导致的溶血，后者
则是一种获得性造血干细胞克隆性疾病，两者常单独发病，伴随或相互继发的病例也可见。在临床诊疗中，阵发性睡眠性血红
蛋白尿样缺陷样缺陷的自身免疫性溶血性贫血是自免溶贫的一种特殊类型，应注意与经典阵发性睡眠性血红蛋白尿样缺陷加
以区分。

Abstract: Both autoimmune hemolytic anemia and paroxysmal nocturnal hemoglobinuria are common hemolytic diseases.
The former causes hemolysis because of immune disorder, and the latter is an acquired clonal hematologic disorder of stem
cells. The two entities are often separate diseases, but can also occur concomitantly or secondary to each other. paroxysmal
nocturnal haemoglobinuria-like defect-like defect is a special type of autoimmune haemolytic anaemia and should be
distinguished from typical paroxysmal nocturnal haemoglobinuria-like defect.