[1]徐夏,邓文婷,黄成志,等.喉部Rosai-Dorfman病1例报道及文献复习[J].南方医科大学学报,2018,(02):125.
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喉部Rosai-Dorfman病1例报道及文献复习()
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《南方医科大学学报》[ISSN:/CN:]

卷:
期数:
2018年02期
页码:
125
栏目:
出版日期:
2018-02-15

文章信息/Info

Title:
Rosai-Dorfman disease in the larynx: report of a case and literature review
作者:
徐夏邓文婷黄成志汪建
关键词:
Rosai-Dorfman病结外组织侵犯手术治疗
Keywords:
Rosai-Dorfman disease extranodal involvement surgical treatment
摘要:
Rosai-Dorfman病是一种发生在淋巴结或结外组织的良性组织细胞增生性病变,而发生在喉部的结外Rosai-Dorfman病 例及其罕见,其病变特征不明显,缺乏典型的发热及淋巴结肿大症状,临床上易误诊为恶性肿瘤,治疗也无标准可循。本文 报道1 例喉部Rosai-Dorfman病,应用微创手术加激素治疗,保留了喉功能,取得良好疗效,并结合文献对这一罕见疾病的诊治 进行探讨。
Abstract:
Rosai-Dorfman disease (RDD) is a rare histiocytic disorder that has nodal and extranodal manifestations. Currently no guidelines are available for the management of this disease. We report a case of laryngeal RDD that did not present with classical symptoms such as fever or lymphadenopathy and could be easily misdiagnosed as malignant tumor. The patient received minimally invasive surgeries combined with steroid therapy to preserve the laryngeal function as much as possible, and a favorable clinical outcome was obtained. Reports of similar cases in literatures were reviewed to obtain a better understanding of the disease course, diagnosis and treatment of this uncommon condition.
更新日期/Last Update: 1900-01-01